Malignant Peripheral Nerve Sheath Tumor Related to Diffuse Neurofibroma of Chest Wall
نویسندگان
چکیده
منابع مشابه
Intrathoracic Malignant Peripheral Nerve Sheath Tumor: Histopathological and Immunohistochemical Features
Malignant peripheral nerve sheath tumor (MPNST) is a rare nerve sheath tumor derived from Schwann cells or pleuripotent cells of neural crest. Neurogenic tumors make about 10-20% of all mediastinal tumors. Incidence of MPNST is 0.001% in general population and 0.16% in patients with neurofibromatosis I (NF I). We report a case of 60 year female presenting with progressive cough and breathlessne...
متن کاملReconstruction of the chest wall after excision of a giant malignant peripheral nerve sheath tumor.
Primary chest wall tumors are uncommon and constitute 0.2-2% of all tumors. Metastatic tumors and tumors of local extension are more common. Malignant peripheral nerve sheath tumor (MPNST) of the chest wall is even rarer and its incidence on the chest wall not stated in the literature. The incidence in the general population is 0.0001% while the risk is approximately 4600 times higher in patien...
متن کاملMalignant Peripheral Nerve Sheath Tumour Arising From Solitary Sclerotic Neurofibroma.
Neurofibroma is a benign neoplasm of the peripheral nerve, which occurs as multiple tumours in neurofibromatosis type 1 (NF1) or as a solitary tumour with no association with NF1. Malignant change is sometimes reported in neurofibroma in NF1, but there are few reports of malignant transformation of solitary neurofibroma. We report here a case of malignant change in a solitary sclerotic neurofib...
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A 40-year-old man presented with complaints of left-sided lower back discomfort for 2 to 3 months. There was no other significant history. Physical examination was unremarkable except for a palpable mass in the left flank. Ultrasonography showed a hypoechoic mass. Biphasic contrast-enhanced computerized tomogram revealed a large, heterogenous, infiltrating, necrotic mass lesion arising from the...
متن کاملMalignant Peripheral Nerve Sheath Tumor in the Maxilla: Report of a Rare Case
Malignant peripheral nerve sheath tumor (MPNST) is a rare malignant tumor that develops either from a preexisting neurofibroma or de novo. The cell of origin is believed to be the Schwann cell and possibly other nerve sheath cells. In this report, we describe a rare case of MPNST that arise from the socket of second left maxillary molar that has been already extracted in a young man. He was ref...
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ژورنال
عنوان ژورنال: Respiratory Case Reports
سال: 2021
ISSN: 2147-2475
DOI: 10.5505/respircase.2021.04696